Pompe disease is a Wigs lysosomal storage disorder in which acid alpha-glucosidase is deficient or absent.Deficiency of this lysosomal enzyme results in progressive expansion of glycogen-filled lysosomes in multiple tissues, with cardiac and skeletal muscle being the most severely affected.The clinical spectrum ranges from fatal hypertrophic cardio
In the process of CO2 geological sequestration, the mechanical properties of coal will be changed after supercritical CO2 interacts with coal.Based on this, in this Foot Care paper, Brazilian splitting test and variable angle shear test were carried out on anthracite under different test conditions, and the changes of tensile strength, shear peak s
Invective metaphors constitute a substantial portion of the metaphorical landscape within the Bulgarian language, and Computer Adaptor likely in other languages as well.This article endeavors to explore Bulgarian invective metaphors from various perspectives, including their vitality, expressiveness, conceptualization schemes, etc.To conduct this r
In this paper, we address key challenges in Proof-of-Stake (PoS) blockchains, with a particular focus on Ethereum 2.0.We introduce an innovative mechanism that combines Tullock contests and signaling games to optimize weight assignments based on security deposits from heterogeneous PRO E2 nodes.While Tullock contests motivate participants to alloca
Better surface finish is believed to be one of the most important benefits of ultrasonic vibration-assisted milling.Many studies have shown that this benefit is most significant during slot-milling of a part when the vibration is applied in feed direction.To explicitly explain this phenomenon, an analytical model is proposed to predict surface roug